Idiopathic Cystic Medial Necrosis of the Aorta.

Idiopathic cystic medionecrosis and aneurysms of the ascending aorta.

SUMMARY Two patients with ascending aortic aneurysms due to cystic medical necrosis are described. One of them was phenotypically normal while the other had features of Marfan's syndrome. Both were disabled by dyspnoea and angina which required corrective surgery.

Healed dissecting aneurysm in cystic medial necrosis of the aorta.

DISSECTING aneurysm of the aorta has long been recognized as a disease entity, and is ordinarily regarded as a rapidly fatal condition. A certain proportion of dissecting aneurysms redissect into the lumen of the aorta, forming the so-called "double-barreled" aorta. Occasional cases of dissecting aneurysm have survived for a considerable period after the acute episode, many of them being of the...

CLINICOPATHOLOGIC CORRELATIONS Spontaneous Laceration of Ascending Aorta

Spontaneous laceration of the ascending aorta may result in (1) through-and-through laceration causing hemopericardium, (2) limited intramural dissection of blood (incomplete dissecting aneurysm), or (3) classical dissecting aneurysm. The latter is the most common manifestation. Background conditions include either extensive cystic medial necrosis (as may be seen in Marfan's syndrome) or hypert...

Association of aortic valvular disease and cystic medial necrosis of the ascending aorta; report of four instances.

Pulmonary arterial disease with multifocal dissecting haemorrhage in a newborn infant

Intramural haemorrhage in pulmonary arteries is very rare and usually takes the form of a dissecting aneurysm in the pulmonary trunk or a major pulmonary artery. It usually develops on the basis of cystic medial necrosis and pulmonary hypertension. We report a newborn infant with congenital heart disease in whom multifocal haemorrhage occurred in the media of elastic and muscular pulmonary arte...